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罗萨伊-多夫曼病

Rosai Dorfman disease.

作者信息

Mazhar Erum, Rahman Naila, Qureshi Hina, Bahar Farkhunda, Zakai Atif, Rahman Arshalooz, Hashmi Khalid Zafar

机构信息

Department of Hematology, Liaquat National Hospital, Karachi.

出版信息

J Coll Physicians Surg Pak. 2004 Mar;14(3):183-4.

Abstract

We report an unusual presentation of sinus histiocytosis with massive lymphadenopathy (SHML), also called Rosai Dorfman disease. The child presented with bilateral proptosis with massive cervical lymphadenopathy. The patient had fair response to steroid therapy but relapsed during the course of the disease.

摘要

我们报告了一例伴有巨大淋巴结病的窦性组织细胞增多症(SHML),也称为罗萨伊-多夫曼病的不寻常表现。该患儿表现为双侧眼球突出伴巨大颈部淋巴结病。患者对类固醇治疗反应良好,但在病程中复发。

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