Mazhar Erum, Rahman Naila, Qureshi Hina, Bahar Farkhunda, Zakai Atif, Rahman Arshalooz, Hashmi Khalid Zafar
Department of Hematology, Liaquat National Hospital, Karachi.
J Coll Physicians Surg Pak. 2004 Mar;14(3):183-4.
We report an unusual presentation of sinus histiocytosis with massive lymphadenopathy (SHML), also called Rosai Dorfman disease. The child presented with bilateral proptosis with massive cervical lymphadenopathy. The patient had fair response to steroid therapy but relapsed during the course of the disease.
我们报告了一例伴有巨大淋巴结病的窦性组织细胞增多症(SHML),也称为罗萨伊-多夫曼病的不寻常表现。该患儿表现为双侧眼球突出伴巨大颈部淋巴结病。患者对类固醇治疗反应良好,但在病程中复发。