Ng Alex W H, Lee Paul S F, Howard Robert G
Department of Diagnostic Radiology and Organ Imaging, Prince of Wales Hospital, Hong Kong, China.
Australas Radiol. 2004 Jun;48(2):211-3. doi: 10.1111/j.1440-1673.2004.01299.x.
Renal primitive neuroectodermal tumour (PNET) is a rare malignant tumour of paediatric patients. We describe the important imaging findings, including the ultrasound, CT and MRI of a case of renal PNET in a teenager. To our knowledge, some findings have not been described previously. Some features that have been considered as characteristic are not present in our case, and it is, to our knowledge, the first documented case with such extensive tumour thrombus. We also demonstrate the importance of including PNET as a differential diagnosis because combined chemotherapy is thought to be the best first-line treatment in most cases. Histological diagnosis can be determined by a minimally invasive procedure instead of laparotomy or open biopsy.
肾原始神经外胚层肿瘤（PNET）是儿科患者中一种罕见的恶性肿瘤。我们描述了一名青少年肾PNET病例的重要影像学表现，包括超声、CT和MRI。据我们所知，一些表现此前尚未被描述。一些被认为具有特征性的表现未出现在我们的病例中，据我们所知，这是首例有如此广泛肿瘤血栓的记录病例。我们还证明了将PNET纳入鉴别诊断的重要性，因为在大多数情况下联合化疗被认为是最佳的一线治疗方法。组织学诊断可通过微创程序而非剖腹手术或开放活检来确定。
