Gu Jiansen, Yu Hong, Zhao Xiaotian, Changqing Tan
Department of Otorhinolaryngology, Affiliated Zhongda Hospital of Southeast University, Nanjing, 210009, China.
Lin Chuang Er Bi Yan Hou Ke Za Zhi. 2004 Apr;18(4):207-8.
To discuss the diagnosis and the therapy methods of congenital temporal bone cholesteatoma.
Reviewing and analyzing the clinical data and information about 16 cases of congenital temporal bone patients from 1980 to 2002.
The surgery were proceeded for removing cholesteatoma focus in all patients and the diagnosing were made by histopathologic investigation. Following for half to three years, 6 cases of facial nerve paralysis got partially or totally healing, hearing function improved in 5 cases, 2 cases relapsed and operation were made again for resecting, recrudescent cholesteatoma. There were no any subsequent symptoms happened.
The diagnosis of congenial temporal bone cholesteatoma mainly base on the patient's clinical symptoms and manifestation, and imaging examination. MRI can clearly show cholesteatoma focus and other organs or tissues (including some encephalic frameworks) around it, which also is one of important inspection techniques for discriminating from congenital encephalic cholesteatoma near rock part of temporal bone. The drum integrity is not necessary condition for diagnosing this disease, the surgery approaches are selected by the size and position of focus. The key for preventing recrudescence is to drastically eliminate cholesteatoma tissues.
探讨先天性颞骨胆脂瘤的诊断及治疗方法。
回顾分析1980年至2002年16例先天性颞骨患者的临床资料。
所有患者均行手术切除胆脂瘤病灶，经组织病理学检查确诊。随访半年至3年，6例面神经麻痹部分或完全恢复，5例听力功能改善，2例复发再次手术切除复发性胆脂瘤，无任何后遗症发生。
先天性颞骨胆脂瘤的诊断主要依据患者的临床症状、体征及影像学检查。MRI能清晰显示胆脂瘤病灶及其周围的其他器官或组织（包括部分脑结构），也是鉴别颞骨岩部附近先天性脑内胆脂瘤的重要检查方法之一。鼓膜完整与否不是诊断本病的必要条件，手术方式根据病灶大小及位置选择。防止复发的关键是彻底清除胆脂瘤组织。
