Sterkers J M, Sterkers O
Ann Otolaryngol Chir Cervicofac. 1980 Jul-Aug;97(7-8):579-89.
The authors report 5 cases of congenital cholesteatoma of the temporal bone where the diagnosis was made earlier in each successive case. The first diagnosis was made on the basis of a total paralysis of the facial nerve, the last was made on the basis of a transitory paralysis of the facial nerve associated in the majority of cases with deafness or reduced hearing. Early removal preserves fonction of the VII and VIIIth nerve and is the justification for a systematic X-ray in the Stenver's incidences to be carried out in any facial weakness even if it is transitory. The surgical approach of choice is the middle fossa approach. There is no drainage necessary because these cholesteatomas are not infected.
作者报告了5例颞骨先天性胆脂瘤病例，每例病例的诊断都较前一例更早。第一例诊断是基于面神经完全麻痹，最后一例是基于面神经短暂麻痹，多数情况下伴有耳聋或听力下降。早期切除可保留VII和VIII神经的功能，这也是对任何面神经麻痹（即使是短暂性的）都要在斯滕弗位进行系统性X线检查的理由。首选的手术入路是中颅窝入路。由于这些胆脂瘤未感染，无需引流。
