隆突性皮肤纤维肉瘤的胰腺转移

Pancreatic metastasis of dermatofibrosarcoma protuberans.

作者信息

Yokoyama Yujiro, Murakami Yoshiaki, Sasaki Masaru, Morifuji Masahiko, Hayashidani Yasuo, Kobayashi Takeshi, Sudo Takeshi, Sueda Taijiro

机构信息

Department of Surgery, Graduate School of Biomedical Sciences, Hiroshima University, 1-2-3 Kasumi, Minami-ku, 734-8551 Hiroshima, Japan.

出版信息

J Gastroenterol. 2004 Aug;39(8):798-800. doi: 10.1007/s00535-004-1376-z.

DOI:10.1007/s00535-004-1376-z

PMID:15338376

Abstract

Dermatofibrosarcoma protuberans (DFSP) is a relatively rare skin tumor that is considered to have intermediate malignancy; it demonstrates frequent local recurrence, but systemic metastasis is rare. We report a 49-year-old woman with pancreatic metastasis of DFSP who underwent total pancreatectomy with partial resection of the portal vein. Except for our patient, only two other cases of pancreatic metastasis of DFSP have been reported in the literature, to our knowledge. Radical resection may be considered for pancreatic metastasis of DFSP when there are no other metastatic lesions.

摘要

隆突性皮肤纤维肉瘤（DFSP）是一种相对罕见的皮肤肿瘤，被认为具有中度恶性；它常出现局部复发，但很少发生全身转移。我们报告了一名49岁患有DFSP胰腺转移的女性患者，该患者接受了全胰切除术及门静脉部分切除术。据我们所知，除了我们的患者外，文献中仅报道了另外两例DFSP胰腺转移的病例。当不存在其他转移病灶时，对于DFSP胰腺转移可考虑行根治性切除术。