Soergel T M, Doering D L, O'connor D
Department of Obstetrics and Gynecology, University of Louisville School of Medicine, Louisville, Kentucky, 40202, USA.
Gynecol Oncol. 1998 Nov;71(2):320-4. doi: 10.1006/gyno.1998.5173.
Dermatofibrosarcoma protuberans (DFSP) of the vulva is a rare, low- to intermediate-grade sarcoma of dermal origin. This case report represents the 13th reported patient with vulvar DFSP and the first reported patient with metastatic vulvar DFSP. Although metastasis is rare, the possibility remains that the frequent recurrence of DFSP will eventually metastasize. Therefore, patients must be followed up on a long-term basis to monitor the progress of this potentially lethal cancer.
外阴隆突性皮肤纤维肉瘤（DFSP）是一种罕见的、低至中度恶性的真皮源性肉瘤。本病例报告是第13例报告的外阴DFSP患者，也是首例报告的转移性外阴DFSP患者。尽管转移罕见，但DFSP频繁复发最终仍有可能发生转移。因此，必须对患者进行长期随访，以监测这种潜在致命癌症的进展情况。
