Chilukuri Durga Sowgandhi, Premkumar Prithviraj, Venkitaraman Balasubramanian, Soundararajan Jagadesh Chandra Bose
General Surgery, Sri Ramachandra Medical College and Research Institute, Chennai, India.
Surgical Oncology, Sri Ramachandra Medical College and Research Institute, Chennai, India.
BMJ Case Rep. 2020 Jan 23;13(1):e232614. doi: 10.1136/bcr-2019-232614.
Dermatofibrosarcoma protuberans (DFSP) is a rare soft tissue malignancy which is locally aggressive, slow growing. It has a very low metastatic potential and has high risk of local recurrence. We report a 65-year-old man with recurrent DFSP of thigh with pancreatic metastasis. Apart from our patient, only four other cases of pancreatic metastasis of DFSP have been reported. Our patient had a solitary metastasis to pancreas and was treated with distal pancreaticosplenectomy. Outcome of the patient was good. We present this case report to emphasise that resection may be considered for solitary metastasis of DFSP and can be managed successfully.
隆突性皮肤纤维肉瘤（DFSP）是一种罕见的软组织恶性肿瘤，具有局部侵袭性、生长缓慢。其转移潜能极低，但局部复发风险高。我们报告了一名65岁男性，患有大腿复发性DFSP并伴有胰腺转移。除我们的患者外，仅另有4例DFSP胰腺转移的病例被报道。我们的患者胰腺有孤立性转移，接受了胰体尾脾切除术治疗。患者预后良好。我们呈现此病例报告以强调对于DFSP的孤立性转移可考虑行手术切除，且能够成功处理。
