Carles D, Serville F, Dubecq J P, Alberti E M, Horovitz J, Weichhold W
Unités de Foetopathologie, Groupe Hospitalier Pellegrin, Bordeaux, France.
Arch Pathol Lab Med. 1992 Mar;116(3):293-5.
We report a case of idiopathic arterial calcification in a stillborn. As usually noted in this rare entity, the pregnancy was complicated by a polyhydramnios. The postmortem examination showed generalized arterial calcification, periarticular calcific deposits, and a large pleural hemorrhage. The causes of fetal hydrops in idiopathic infantile calcification are discussed, and, in the present case, the absence of myocardial ischemic lesion suggests that the fetal hydrops and the fetal death could have been caused by the bulky blood clot that was present in the right pleural cavity. The pathogenesis remains undetermined, but a primitive inherent defect of the elastic elements seems to initiate this disorder.
我们报告一例死产儿特发性动脉钙化病例。正如在这种罕见病症中通常所观察到的那样,该妊娠合并羊水过多。尸检显示全身性动脉钙化、关节周围钙化沉积以及大量胸腔出血。本文讨论了特发性婴儿钙化中胎儿水肿的原因,在本病例中,心肌缺血性病变的缺失表明胎儿水肿和胎儿死亡可能是由右胸腔内存在的巨大血凝块所致。发病机制尚不清楚,但弹性元件的原始固有缺陷似乎引发了这种病症。