Fukuzumi Yoko, Oi Shizuo, Matsubara Osamu, Kaito Nobuyoshi, Tani Satoshi, Abe Toshiaki
Department of Neurosurgery, Jikei University School of Medicine, 3-25-8 Nishi-shinbashi Minatoku, 105-8461, Tokyo, Japan.
Childs Nerv Syst. 2005 Mar;21(3):244-8. doi: 10.1007/s00381-004-1000-9. Epub 2004 Sep 15.
The authors report a case of isolated atlas hypoplasia in an 18-month-old infant who experienced delayed motor development confined to the lower extremities, in the absence of other clinical features. Nonetheless, MRI revealed the upper cervical cord to be highly compressed with a high signal intensity lesion apparent at the craniovertebral junction. The patient underwent atlas laminectomy in addition to occipital decompression, resulting in a good neurological recovery.
We speculate on the significance of this unique clinical presentation and discuss surgical strategies for this condition.
作者报告了一例18个月大婴儿的孤立性寰椎发育不全病例,该婴儿存在仅局限于下肢的运动发育迟缓,且无其他临床特征。尽管如此,磁共振成像(MRI)显示颈髓上段受到高度压迫,在颅颈交界处可见高信号强度病变。该患者除进行枕下减压外,还接受了寰椎椎板切除术,术后神经功能恢复良好。
我们推测了这种独特临床表现的意义,并讨论了针对该病症的手术策略。