Mannan Abul Ala Syed Rifat, Ray Ruma, Sharma Suresh C, Hatimota Pradeep
Department of Pathology, All India Institute of Medical Sciences, New Delhi, India.
Ear Nose Throat J. 2004 Jul;83(7):481-4.
Infantile fibromatosis is an uncommon, usually cutaneous, nonmetastasizing but locally aggressive fibroblastic proliferation. Involvement of the sinonasal area is extremely uncommon, and only 5 cases have been previously reported. We report a new case, which occurred in a 2-year-old boy. The mass involved the nasal cavity and the paranasal sinuses and extended into the cranial cavity. We also discuss the clinicopathologic features of this lesion, including its ultrastructural characteristics, and we review the literature.
婴儿纤维瘤病是一种罕见的、通常累及皮肤的、不发生转移但具有局部侵袭性的成纤维细胞增生性疾病。鼻窦区域受累极为罕见,此前仅有5例报道。我们报告1例新病例,发生于一名2岁男孩。肿块累及鼻腔和鼻窦,并延伸至颅腔。我们还讨论了该病变的临床病理特征,包括其超微结构特征,并对文献进行了综述。