Dalit Amar, Karen Meir, Alexander Margulis
Department of Plastic and Reconstructive Surgery, Hadassah Medical Organization, Jerusalem, Israel.
Eplasty. 2009 Nov 10;9:e52.
Desmoid tumors are rare benign neoplasms of fibroblastic origin, frequently presenting in the abdomen of adult patients. Little is reported about clinical features and outcome of desmoid tumors appearing in infants and children, especially when they are located in the face.
We report a girl with a desmoid tumor of her cheek, which was present at birth.
The tumor was treated by surgical excision, with no additional treatment, other than follow-up. No recurrence of the tumor was witnessed 15 months following surgical excision.
Radical surgical treatment with tumor excision, sometimes accompanied by radiotherapy, is the current standard therapy for infantile desmoid tumors. Pharmacological treatment may be added in selected cases. These modalities may be challenging when desmoid tumors appear in the face because of risks of facial distortion and associated growth problems.
韧带样瘤是一种罕见的起源于成纤维细胞的良性肿瘤，常见于成年患者的腹部。关于婴儿和儿童韧带样瘤的临床特征及预后报道较少，尤其是位于面部的此类肿瘤。
我们报告一名出生时即患有脸颊韧带样瘤的女孩。
该肿瘤通过手术切除进行治疗，术后除随访外未进行其他治疗。手术切除15个月后未见肿瘤复发。
肿瘤切除的根治性手术治疗，有时联合放疗，是目前婴儿韧带样瘤的标准治疗方法。在某些特定病例中可加用药物治疗。当韧带样瘤出现在面部时，由于存在面部畸形和相关生长问题的风险，这些治疗方式可能具有挑战性。
