Napolitano Marcello, Righini Andrea, Zirpoli Salvatore, Rustico Mariangela, Nicolini Umberto, Triulzi Fabio
Department of Radiology and Neuroradiology, Childrens Hospital V. Buzzi, Istituti Clinici di Perfezionamento, Milan, Italy.
J Comput Assist Tomogr. 2004 Nov-Dec;28(6):762-5. doi: 10.1097/00004728-200411000-00006.
Rhombencephalosynapsis (RES) is a rare congenital abnormality characterized by vermian agenesis and fusion of the cerebellar hemispheres. In the 3 cases reported here, prenatal magnetic resonance imaging clearly depicted cerebellar features characteristic of RES, allowing a definite diagnosis.