Sebbag G, Sugarbaker P H, Walfisch S, Levy I
Surgery B, Soroka University Medical Center, Ben Gurion University of the Negev, Beer Sheva, Israel.
Scand J Gastroenterol. 2004 Nov;39(11):1172-4. doi: 10.1080/00365520410003623.
Pseudomyxoma peritonei syndrome (PMP) is a rare but fascinating entity in surgical oncology. It consists of the accumulation of mucus in the peritoneal cavity, sometimes in huge amounts, in most of the cases after rupture of an appendiceal tumor. The diagnosis and management of PMP has changed significantly in the past 15 years, with the institution of an aggressive therapeutic combination: cytoreductive surgery and intraperitoneal perioperative chemotherapy. Few reports deal with the late manifestations and complications at endstage of the disease. The cases presented here are unique in that they illustrate a late 'failure' in the perianal area in three patients with long-term PMP.
腹膜假黏液瘤综合征（PMP）是外科肿瘤学中一种罕见但引人关注的病症。它表现为腹腔内黏液积聚，有时量很大，多数情况下是阑尾肿瘤破裂后所致。在过去15年里，PMP的诊断和治疗发生了显著变化，出现了一种积极的联合治疗方法：减瘤手术和围手术期腹腔内化疗。很少有报告涉及该疾病终末期的晚期表现和并发症。这里呈现的病例很独特，因为它们展示了3例长期患有PMP的患者在肛周区域出现的晚期“衰竭”情况。
