Dejong C H, Booster M H, Theunissen P H, Beets G L, van Duin C J
Afd. Algemene Heelkunde, De Wever Ziekenhuis, Heerlen.
Ned Tijdschr Geneeskd. 1997 Jun 14;141(24):1196-8.
Pseudomyxoma peritonei was diagnosed in 3 men aged 38, 66 and 54 years with weight loss and distension of the abdomen. Pseudomyxoma peritonei results from seeding of the peritoneal cavity with mucus-producing epithelium. The disease is traditionally characterized by accumulation of huge amounts of mucinous ascites, relatively long survival and absence of distant, extraperitoneal metastases. Mostly, the primary tumour is an appendicular adenoma or adenocarcinoma. Sometimes, the primary tumor is localized in the ovaries. Extensive surgical debulking with postoperative intraperitoneal chemotherapy appears to be the treatment of choice.
3名年龄分别为38岁、66岁和54岁的男性被诊断为腹膜假黏液瘤，伴有体重减轻和腹部膨隆。腹膜假黏液瘤是由产生黏液的上皮细胞种植于腹膜腔引起的。传统上，该疾病的特征是大量黏液性腹水积聚、生存期相对较长且无远处腹膜外转移。大多数情况下，原发性肿瘤为阑尾腺瘤或腺癌。有时，原发性肿瘤位于卵巢。广泛手术减瘤并术后腹腔内化疗似乎是首选的治疗方法。
