[Congenital glomerular nephropathies].

Congenital glomerulopathies are rare but very severe diseases from the clinical point of view. Their origin is either located in the kidney itself or outside the kidneys. The exact differential diagnosis is only possible taking into consideration other organ systems. A histological certification is mostly inevitable. The prognosis of congenital glomerulopathies is usually bad due to the development of chronic renal failure in most cases. Therapeutic aspects are limited to a small number of specific forms. Recurrences in a renal graft, however, are usually not to be expected.