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在强直性肌营养不良中经鼻面罩使用机械通气

The use of mechanical ventilation via a nasal mask in myotonic dystrophy.

作者信息

Jubran A, D'Alonzo G E, Tobin M J

机构信息

Division of Pulmonary and Critical Care Medicine, Edward Hines Jr, Veterans Administration Hospital, Hines, Ill. 60141.

出版信息

Tex Med. 1992 Feb;88(2):73-5.

PMID:1557716
Abstract

A 36-year-old woman with myotonic dystrophy presented with generalized weakness and daytime somnolence. Arterial blood gas analysis revealed significant hypoxemia and hypercapnia, and a polysomnogram revealed additional oxygen desaturation during sleep. For nocturnal ventilatory assistance, the patient received positive-pressure ventilation via a nasal mask. This mode of ventilation produced marked improvement in the patient's nocturnal hypoxemia.

摘要

一名36岁的强直性肌营养不良女性患者出现全身无力和日间嗜睡症状。动脉血气分析显示存在明显的低氧血症和高碳酸血症,多导睡眠图显示睡眠期间有额外的氧饱和度下降。为进行夜间通气辅助,患者通过鼻罩接受正压通气。这种通气模式使患者夜间低氧血症有了显著改善。

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