Orazi Attilio, O'Malley Dennis P, Jiang Jiazhong, Vance Gail H, Thomas Janice, Czader Magdalena, Fang Wei, An Caroline, Banks Peter M
Department of Pathology and Laboratory Medicine, Indiana University School of Medicine, Indianapolis, Indiana 46202-5200, USA.
Mod Pathol. 2005 May;18(5):603-14. doi: 10.1038/modpathol.3800348.
The WHO criteria for diagnosing acute panmyelosis with myelofibrosis are somewhat distinct from those for acute megakaryoblastic leukemia. However, clinical and hematopathologic findings partially overlap. This has raised questions as to whether these are indeed separate, definable entities. To determine the potential importance of bone marrow biopsy supplemented by immunohistochemistry in distinguishing between these two conditions, we studied 17 bone marrow biopsies of well-characterized cases of acute panmyelosis with myelofibrosis (six cases) and acute megakaryoblastic leukemia (11 cases). We compared blast frequency, reticulin content, CD34 expression, and the degree of megakaryocytic differentiation of the blast cells in these two conditions. Our results demonstrate important differences. Acute panmyelosis with myelofibrosis is characterized by a multilineage myeloid proliferation with a less numerous population of blasts than acute megakaryoblastic leukemia (P<0.01). In the former condition, blasts are always positive with CD34, while in acute megakaryoblastic leukemia they express CD34 in 60% of the cases. The blasts in acute panmyelosis with myelofibrosis only rarely express megakaryocytic antigens. By contrast, acute megakaryoblastic leukemia has a significantly higher proportion of blasts expressing megakaryocytic antigens (P<0.01 with CD42b). Our results confirm that histology supplemented by immunohistochemistry permits the distinction of these conditions in routinely processed bone marrow biopsies.
世界卫生组织(WHO)诊断伴骨髓纤维化的急性全髓增殖症的标准与急性巨核细胞白血病的标准有所不同。然而,临床和血液病理学表现部分重叠。这引发了关于它们是否确实是独立的、可定义的实体的疑问。为了确定骨髓活检辅以免疫组织化学在区分这两种疾病中的潜在重要性,我们研究了17例伴骨髓纤维化的急性全髓增殖症(6例)和急性巨核细胞白血病(11例)的特征明确的骨髓活检标本。我们比较了这两种情况下原始细胞频率、网状纤维含量、CD34表达以及原始细胞的巨核细胞分化程度。我们的结果显示出重要差异。伴骨髓纤维化的急性全髓增殖症的特征是多系髓系增殖,与急性巨核细胞白血病相比原始细胞数量较少(P<0.01)。在前一种情况下,原始细胞CD34总是呈阳性,而在急性巨核细胞白血病中,60%的病例原始细胞表达CD34。伴骨髓纤维化的急性全髓增殖症中的原始细胞很少表达巨核细胞抗原。相比之下,急性巨核细胞白血病中表达巨核细胞抗原的原始细胞比例显著更高(CD42b检测时P<0.01)。我们的结果证实,在常规处理的骨髓活检中,组织学辅以免疫组织化学能够区分这些疾病。