Maàmouri N, Cheikh I, Ouerghi H, Oukaà A, Belkahla N, Mnif E, Hechiche M, Driss M, Ben Ammar A
Service de gastroentérologie B, hôpital La-Rabta, 1007 Tunis Jebbari, Tunisie.
Rev Med Interne. 2005 Feb;26(2):145-8. doi: 10.1016/j.revmed.2004.10.029.
Retroperitoneal Liposarcoma is a rare and primary malignancy developed from mesenchymal tissue. It's generally unique and shows an only one histologic component. We report a case of multicentric and synchronous liposarcoma (intraperitoneal and retroperitoneal) and with different histologic types.
A 53-year old man presented with abdominal pain, increased abdominal girth and weight loss. Physical examination revealed two abdominal masses. Computed tomography scan showed a very large retroperitoneal mass displacing the left kidney, digestive loops and vessels. The patient underwent surgery. One enormous mass of the left renal lodge measuring 50 cm, a retroduodenal mass measuring 15 cm and a nodule of the coecum were removed. Histological examination of the mass of the left renal lodge revealed mixed type liposarcoma (dedifferentiated and myxoid). Histological examination of the retroduodenal mass and of the nodule of the coecum revealed well-differentiated liposarcoma.
Pathological, therapeutic and prognostic aspects of abdominal liposarcoma will be reviewed in this article.
腹膜后脂肪肉瘤是一种罕见的起源于间叶组织的原发性恶性肿瘤。它通常较为独特，仅表现为一种组织学成分。我们报告一例多中心同步脂肪肉瘤（腹腔内和腹膜后）且具有不同组织学类型的病例。
一名53岁男性，出现腹痛、腹围增大和体重减轻症状。体格检查发现腹部有两个肿块。计算机断层扫描显示一个非常大的腹膜后肿块，推移了左肾、消化袢和血管。患者接受了手术。切除了一个位于左肾窝的巨大肿块（大小为50厘米）、一个位于十二指肠后的肿块（大小为15厘米）以及一个盲肠结节。对左肾窝肿块的组织学检查显示为混合型脂肪肉瘤（去分化型和黏液型）。对十二指肠后肿块和盲肠结节的组织学检查显示为高分化脂肪肉瘤。
本文将对腹部脂肪肉瘤的病理、治疗和预后方面进行综述。
