Ferraro G A, Perrotta A, Rossano F, D'Andrea F
Aesthetic Plast Surg. 2005 Jan-Feb;29(1):32-3. doi: 10.1007/s00266-004-0047-z. Epub 2005 Mar 10.
Poland syndrome comprises a unilateral absence of the large pectoral muscle, ipsilateral symbrachydactyly, and occasionally other malformations of the anterior chest wall and breast. The condition is more frequent among males, and usually occurs on the right hemithorax in the unilateral form. The syndrome is believed to be caused by a genetic disorder that reduces the embryonal circulation in the interior chest artery: the stronger the interaction, the more severe the pathology. This article analyzes an unusual pathologic case in which the 17-year-old patient lacked the large pectoral muscle on the left side, but showed no arterial alteration. This case raises questions as to the true pathogenesis of this syndrome.
波兰综合征包括单侧胸大肌缺如、同侧短指并指畸形，偶尔还伴有前胸壁和乳房的其他畸形。这种疾病在男性中更为常见，单侧形式通常发生在右半胸。该综合征被认为是由一种导致胸廓内动脉胚胎循环减少的遗传疾病引起的：相互作用越强，病理变化就越严重。本文分析了一例罕见的病理病例，一名17岁患者左侧胸大肌缺如，但未发现动脉改变。该病例引发了关于该综合征真正发病机制的疑问。
