Gonzalvez Gasch Asunción María, Mirete Ferrer Carlos, Laveda Cano Raquel, Satorres Rosas Javier
Department of Internal Medicine, San Jaime Hospital, Torrevieja, Alicante, Spain.
JOP. 2005 Mar 10;6(2):172-7.
Pancreatic cysts may be incidentally detected in asymptomatic patients evaluated for other clinical manifestations. Microcystic adenomas are particularly rare among pancreatic cyst neoplasms. They are benign lesions and can present as solitary pancreatic tumors or as a radiological manifestation combined with other cystic and tumoral lesions affecting different organs.
A 50-year-old man presented with hematuria. A computed tomography scan of the abdomen showed a 9-centimeter renal mass in the left kidney consistent with a renal-cell carcinoma as well as a cystic lesion the head of the pancreas. The histopathological study of the cystic mass, following a computed tomography guided biopsy, showed a microcystic adenoma. Therefore, further studies were performed so as to assess the relationship between both lesions and determine the final diagnosis.
Microcystic adenomas are exceedingly rare tumors among pancreatic cysts. The combination of a solid renal mass and a pancreatic cystic lesion should lead to a broad differential diagnosis. Pancreatic magnetic resonance imaging has been proven to be particularly useful in evaluating cystic masses. The presence of walls and internal septations in the pancreatic mass with gadolinium enhancement should raise the possibility of an underlying Von Hippel-Lindau syndrome.
胰腺囊肿可能在因其他临床表现接受评估的无症状患者中偶然被发现。微囊性腺瘤在胰腺囊肿性肿瘤中尤为罕见。它们是良性病变,可表现为孤立性胰腺肿瘤,或作为一种影像学表现,与影响不同器官的其他囊性和肿瘤性病变合并出现。
一名50岁男性出现血尿。腹部计算机断层扫描显示左肾有一个9厘米的肾肿块,符合肾细胞癌表现,同时胰腺头部有一个囊性病变。在计算机断层扫描引导下对囊性肿块进行活检后,组织病理学研究显示为微囊性腺瘤。因此,进行了进一步研究,以评估这两种病变之间的关系并确定最终诊断。
微囊性腺瘤在胰腺囊肿中是极为罕见的肿瘤。实性肾肿块和胰腺囊性病变同时出现应进行广泛的鉴别诊断。胰腺磁共振成像已被证明在评估囊性肿块方面特别有用。胰腺肿块中出现壁和内部间隔且钆增强,应提高存在潜在的冯·希佩尔-林道综合征的可能性。