Rho Young Hee, Choi Seong Jae, Choi Youn Seon, Lee Young Ho, Ji Jong Dae, Song Gwan Gyu
Division of Rheumatology, Korea University Guro Hospital, Seoul, South Korea.
J Rheumatol. 2005 May;32(5):954-6.
Relapsing polychondritis is a multisystemic disease of unknown etiology that mainly involves the cartilaginous portions of the ear, nose, and trachea. Occasionally, there is involvement of the cardiovascular system, which usually results in severe morbidity and mortality. The most common manifestation of cardiovascular involvement is aortic root dilation resulting in aortic regurgitation. We describe the first case in Korea, a 51-year-old woman with relapsing polychondritis with aortitis, but without aortic valve involvement. She presented only with complaints of abdominal pain, and was successfully treated with corticosteroids and methotrexate.
复发性多软骨炎是一种病因不明的多系统疾病，主要累及耳、鼻和气管的软骨部分。偶尔会累及心血管系统，这通常会导致严重的发病率和死亡率。心血管受累最常见的表现是主动脉根部扩张导致主动脉瓣关闭不全。我们描述了韩国的首例病例，一名51岁患有复发性多软骨炎合并主动脉炎但未累及主动脉瓣的女性。她仅表现为腹痛，经皮质类固醇和甲氨蝶呤治疗成功。
