Selim A G, Fulford L G, Mohiaddin R H, Sheppard M N
Department of Histopathology, Royal Brompton Hospital, Imperial College, School of Medicine, Sydney Street, London SW3 6NP, UK.
J Clin Pathol. 2001 Nov;54(11):890-2. doi: 10.1136/jcp.54.11.890.
Relapsing polychondritis (RP) is a rare inflammatory multiorgan disorder affecting cartilaginous structures and other connective tissues. Serious cardiovascular complications have been reported in patients with RP, the most frequent being aortic or mitral regurgitation and aortic aneurysms. Aortitis is a very rare complication. An unusual case of active aortitis in a patient with RP, despite intensive immunosuppressive treatment, is described with a special emphasis on the pathological findings.
复发性多软骨炎(RP)是一种罕见的炎症性多器官疾病,会影响软骨结构和其他结缔组织。已有报道称RP患者会出现严重的心血管并发症,最常见的是主动脉或二尖瓣反流以及主动脉瘤。主动脉炎是一种非常罕见的并发症。本文描述了一例RP患者发生活动性主动脉炎的不寻常病例,尽管进行了强化免疫抑制治疗,但特别强调了病理检查结果。