Goto Tomoyuki, Kobayashi Junjiro, Nakajima Hiroyuki, Niwaya Kazuo, Tagusari Osamu, Kitamura Soichiro
Department of Cardiovascular Surgery, National Cardiovascular Center, Osaka, Japan.
Asian Cardiovasc Thorac Ann. 2005 Jun;13(2):181-3. doi: 10.1177/021849230501300219.
A 48-year-old man presented with typical features of Ehlers-Danlos syndrome, such as soft and hyperextensible skin, subcutaneous nodules, clubbed feet, and a mild degree of pigeon chest. In addition, his past history revealed congenital dislocation of the hip joint, retinal detachment, and repeated episodes of congestive heart failure due to severe mitral regurgitation and atrial fibrillation. We subjected the patient to surgical repair of the mitral valve combined with the maze procedure, which proved successful.
