Department of Cardiac Surgery, Heart Center Leipzig, University of Leipzig, Leipzig, Germany.
Ann Thorac Surg. 2010 Jan;89(1):273-5. doi: 10.1016/j.athoracsur.2009.06.033.
Herein, we present an unusual case of a 48-year-old patient with Ehlers-Danlos syndrome (classic type) with multiple cardiovascular pathologies, including mitral regurgitation, a dilated aortic root, and chronic atrial fibrillation. A complex mitral valve repair, modified cryo-Maze procedure, and aortic valve-sparing operation (reimplantation) were performed, which were further complicated by the patient's fragile tissues. The patient was discharged on postoperative day 10 in good health with normal mitral and aortic valve function. We believe that this is the first report of such an extensive cardiac procedure in a patient with Ehlers-Danlos syndrome.
在此，我们报告 1 例 48 岁埃勒斯-当洛斯综合征（经典型）患者，该患者合并多种心血管病变，包括二尖瓣反流、升主动脉扩张和慢性心房颤动。行复杂二尖瓣修复、改良冷冻迷宫术和主动脉瓣保留手术（再植入术），但由于患者组织脆弱，手术进一步复杂化。患者术后第 10 天健康出院，二尖瓣和主动脉瓣功能正常。我们认为，这是首例此类广泛心脏手术在埃勒斯-当洛斯综合征患者中的报告。
