Jacquemin G, Laloux P
Department of General Surgery, Hospital Centre of Dinant, Belgium.
Acta Chir Belg. 2005 Apr;105(2):127-33.
Pseudomyxoma peritonei is an uncommon condition characterized by abundant extracellular mucinous material and peritoneal tumoural implants. A ruptured appendiceal mucinous adenoma seems to be the most common origin, but low grade ovarian malignancies are often associated. Peritoneal gelatinous diseases must be subdivided into disseminated peritoneal adenomucinosis, peritoneal mucinous carcinomatosis and intermediate cases. These entities have significantly different prognosis. Debulking surgery is the most common treatment but some are in favour of an ultra radical surgery with hyperthermic intra-peritoneal chemotherapy, with some encouraging results.
腹膜假黏液瘤是一种罕见疾病，其特征为大量细胞外黏液物质和腹膜肿瘤种植。阑尾黏液性腺瘤破裂似乎是最常见的起源，但低级别卵巢恶性肿瘤也常与之相关。腹膜胶冻样疾病必须细分为播散性腹膜腺黏液瘤病、腹膜黏液性癌病及中间型病例。这些实体的预后有显著差异。肿瘤细胞减灭术是最常见的治疗方法，但有些人支持采用腹腔内热灌注化疗的超根治性手术，且取得了一些令人鼓舞的结果。
