Brueggen Carol, Baird Gayle, Meisheid Allison
College of Medicine, Mayo Clinic, Rochester, MN, USA.
Clin J Oncol Nurs. 2007 Aug;11(4):525-32. doi: 10.1188/07.CJON.525-532.
Pseudomyxoma peritonei (PMP) syndrome is an uncommon, slowly progressive condition that usually arises from perforation of an adenoma in the appendix. PMP syndrome is characterized by mucin accumulation in the peritoneal cavity. Mucinous implants are found on all peritoneal surfaces and the omentum. PMP syndrome rarely metastasizes outside the abdominal cavity but remains a fatal illness as the space in the abdomen and pelvis required for normal function of the gastrointestinal tract becomes filled with copious amounts of the mucinous tumor. Treatment options include observation, aggressive debulking surgery, intraperitoneal chemotherapy, radiotherapy, and mucolytic agents.
腹膜假黏液瘤（PMP）综合征是一种罕见的、进展缓慢的疾病，通常由阑尾腺瘤穿孔引起。PMP综合征的特征是腹腔内黏液积聚。在所有腹膜表面和大网膜上都可发现黏液性种植体。PMP综合征很少转移至腹腔外，但仍是一种致命疾病，因为胃肠道正常功能所需的腹部和盆腔空间会被大量黏液性肿瘤填满。治疗选择包括观察、积极的减瘤手术、腹腔内化疗、放疗和黏液溶解剂。
