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Palatal myoclonus: an unusual presentation.

作者信息

Ross Shelly, Jankovic Joseph

机构信息

Parkinson's Disease Center and Movement Disorders Clinic, Department of Neurology, Baylor College of Medicine, Houston, Texas 77030, USA.

出版信息

Mov Disord. 2005 Sep;20(9):1200-3. doi: 10.1002/mds.20516.

DOI:10.1002/mds.20516
PMID:15929094
Abstract

We describe a 16-year-old woman with an unusual clinical presentation of palatal myoclonus after a severe upper respiratory infection. Besides the postinfectious onset, this case is unique in that the rhythmical contractions of her oropharynx, larynx, and esophagus occur in couplets rather than single contractions of typical essential palatal myoclonus. Additionally, these contractions are present only during the inspiratory phase of respiration. Imaging and other diagnostic studies show no evidence of cerebellar or brainstem pathology. This case broadens the phenomenology of palatal myoclonus and illustrates the occasional overlap in clinical features between essential and symptomatic palatal myoclonus.

摘要

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