Ozokutan Bülent Hayri, Küçükaydin Mustafa, Ceylan Haluk, Gözüküçük Ali, Karaca Fahri
Department of Pediatric Surgery, Gaziantep University Medical Faculty, Gaziantep, Turkey.
Int J Urol. 2005 Apr;12(4):419-21. doi: 10.1111/j.1442-2042.2005.01055.x.
Congenital megalourethra is a rare congenital malformation of the penile urethra. It is defined as the diffuse dilatation of the anterior urethra due to the absence of development of the erectile tissue of the penis. Since the initial description, nearly 80 cases with megalourethra have been reported in English literature. Congenital megalourethra has been classified into scaphoid and fusiform types and is usually associated with additional urinary tract and other system anomalies, irrespective of its type and severity. We report two rare cases of scaphoid megalourethra without any associated anomaly. A 13-year-old boy and an 8-month-old boy were admitted to the Department of Pediatric Surgery with complaints of penile swelling and dysuria since birth. Physical examination and retrograde cystourethrogram confirmed the diagnosis of congenital scaphoid megalourethra. Both patients underwent a reduction urethroplasty. They did well postoperatively and voided with a normal stream without any abnormality of the penile shaft.
先天性巨尿道是一种罕见的阴茎尿道先天性畸形。它被定义为由于阴茎勃起组织发育缺失导致前尿道弥漫性扩张。自最初描述以来,英文文献中已报道了近80例巨尿道病例。先天性巨尿道已被分为舟状和梭形类型,并且通常与其他泌尿系统及其他系统异常相关,无论其类型和严重程度如何。我们报告两例罕见的无任何相关异常的舟状巨尿道病例。一名13岁男孩和一名8个月大男孩因自出生以来阴茎肿胀和排尿困难而入住小儿外科。体格检查和逆行膀胱尿道造影证实了先天性舟状巨尿道的诊断。两名患者均接受了尿道缩窄成形术。他们术后恢复良好,排尿顺畅,阴茎干无任何异常。