Franga Dion L, Howell Charles G, Mellinger John D, Hatley Robyn M
Department of Surgery, Medical College of Georgia, Augusta, GA 30912, USA.
Am Surg. 2005 May;71(5):398-401.
Choledochal cysts represent a rare disease in the Western world. We reviewed our recent experience with a case of perforated choledochal cyst, define the currently accepted treatment options, and review the literature of this unusual disease. An 11-month-old girl presented with abdominal pain and distention as well as non-bilious vomiting. Subsequent workup included endoscopic retrograde cholangiopancreatography revealing a perforated type I choledochal cyst. She underwent single-stage excision and reconstruction with a Roux-en-Y hepaticojejunostomy. Perforated choledochal cyst is a rare event, and prompt surgical intervention is warranted. Single-stage cystectomy and Roux-en-Y reconstruction is possible in select patients. A thorough understanding of the pathophysiology, management, and follow-up is required.
胆总管囊肿在西方世界是一种罕见疾病。我们回顾了近期处理一例穿孔性胆总管囊肿的经验，明确了目前公认的治疗方案，并复习了有关这种罕见疾病的文献。一名11个月大的女童出现腹痛、腹胀以及非胆汁性呕吐。后续检查包括内镜逆行胰胆管造影，结果显示为I型穿孔性胆总管囊肿。她接受了一期囊肿切除并采用Roux-en-Y肝空肠吻合术进行重建。穿孔性胆总管囊肿是一种罕见情况，需要及时进行手术干预。在部分患者中可行一期囊肿切除术和Roux-en-Y重建术。需要对其病理生理学、治疗及随访有全面的了解。
