Alehan Dursun, Dogan Omer Faruk
Division of Pediatric Cardiology, Hacettepe University Faculty of Medicine, Sihhiye, Ankara, Turkey.
Cardiol Young. 2005 Aug;15(4):434-6. doi: 10.1017/S1047951105000910.
Ventricular noncompaction is a rare unclassified cardiomyopathy occurring because of arrest of the normal intrauterine compaction of the loose luminal component of the ventricular myocardium. There is limited data regarding its diagnosis and outcome in children. It is recognised, however, that right ventricular involvement is extremely rare. We report a case in which only the right ventricular myocardium was noncompacted, a situation which led to heart failure soon after birth.
心室致密化不全是一种罕见的未分类心肌病，由于胎儿期心室心肌疏松腔内容物正常致密化过程停滞所致。关于其在儿童中的诊断和预后的数据有限。然而，人们认识到右心室受累极为罕见。我们报告一例仅右心室心肌致密化不全的病例，这种情况在出生后不久即导致心力衰竭。
