Sert Ahmet, Aypar Ebru, Aslan Eyup, Odabas Dursun
Department of Pediatric Cardiology, Konya Training and Research Hospital, 42080, Konya, Turkey,
Pediatr Cardiol. 2013;34(8):1896-8. doi: 10.1007/s00246-012-0435-0. Epub 2012 Jul 19.
Noncompaction of the ventricular myocardium is a rare cardiomyopathy characterized by a pattern of prominent trabecular meshwork and deep intertrabecular recesses. The prevalence of left ventricular noncompaction is 0.01% in adults and 0.14% in pediatric patients. Although the usual site of involvement is the left ventricle, the right ventricle and septum can be affected as well. Previously, right ventricular noncompaction has been described only in a few cases of newborns with congenital heart defects and in adult patients. This report presents a newborn with isolated right ventricular noncompaction. To the authors' knowledge, this is the first newborn patient with isolated right ventricular noncompaction but no congenital heart defect involving only the right ventricle.
心室心肌致密化不全是一种罕见的心肌病，其特征是存在突出的小梁网状结构和深陷的小梁间隐窝。左心室致密化不全在成人中的患病率为0.01%，在儿科患者中为0.14%。虽然通常受累部位是左心室，但右心室和室间隔也可能受到影响。此前，右心室致密化不全仅在少数患有先天性心脏病的新生儿和成年患者中被描述过。本报告介绍了一名患有孤立性右心室致密化不全的新生儿。据作者所知，这是首例仅患有孤立性右心室致密化不全且无先天性心脏病（仅累及右心室）的新生儿患者。
