Jørgensen P H, Pedersen C B, Hougaard K
Randers Centralsygehus, Ortopaedkirurgisk afdeling.
Ugeskr Laeger. 1992 Apr 20;154(17):1189-90.
We present monozygotic twin girls with bilateral epiphyseal dysplasia of the femoral head (DECF). DECF is a rare condition reported mainly in boys before the age of five years. It consists of a state of non-ossification characterized by flattening and fragmentation of the femoral head. It is invariably followed by 100% healing. The differential diagnosis is primarily from Legg-Calvé-Perthes' disease (LCPD), which, however, occurs mainly after the fifth year followed by aggravation of the symptoms during the following 18 months. This condition leads to secondary degenerative changes in several hips. Although DECF and LCPD may be two entities of the same disease it is necessary to distinguish clinically between them, as the prognosis and the treatment are different.
我们报告了一对患有双侧股骨头骨骺发育异常（DECF）的单卵双胞胎女孩。DECF是一种罕见病症，主要报道于5岁前的男孩。它表现为一种非骨化状态，其特征是股骨头扁平及碎裂。它总会100%愈合。鉴别诊断主要需与Legg-Calvé-Perthes病（LCPD）区分，然而，LCPD主要发生在5岁之后，且在接下来的18个月内症状会加重。这种病症会导致多个髋关节出现继发性退行性改变。尽管DECF和LCPD可能是同一种疾病的两种类型，但由于预后和治疗方法不同，临床上有必要对它们进行区分。
