Gómez García I, González Chamorro F, Fernández Fernández E, Palacio España A, Molina Burgos R, Alvarez E, Conde Someso S
Servicio de Urología, Hospital San Rafael, Madrid.
Actas Urol Esp. 2005 Jun;29(6):603-6. doi: 10.1016/s0210-4806(05)73305-2.
The primary bladder amiloidosis is an uncommon pathology, not existing in the world more than 150 published cases, being even more exceptional the secondary bladder amiloidosis being described around 25 cases. The secondary bladder amiloidosis associates in most from the patients to arthritis reumatoide of long evolution. The diagnoses clinical it is difficult, being necessary the differential diagnosis with the bladder tumour. The pathological study and inmunohistochemics, confirm the diagnosis. We present the case of a patient that I debut with frank hematuria, hemodynamic uncertainty and renal inadequacy that it required combined treatment, doctor and surgical for the resolution of their square.
原发性膀胱淀粉样变性是一种罕见的病理情况，全球已发表病例不超过150例，继发性膀胱淀粉样变性更为罕见，仅有约25例报道。继发性膀胱淀粉样变性在大多数患者中与长期的类风湿性关节炎相关。临床诊断困难，需要与膀胱肿瘤进行鉴别诊断。病理研究和免疫组织化学检查可确诊。我们报告一例患者，其首发症状为明显血尿、血流动力学不稳定和肾功能不全，需要联合药物和手术治疗以解决问题。
