Benito Priscila, Fernández Isabel, Pérez-Carral Jose Ramón, Fernández-Pello Sergio, Cruceyra Guillermo, Menéndez Carmen Luz
Pathology and Urology Department, Hospital de Cabueñes, Gijón, Asturias, Spain.
Arch Esp Urol. 2012 Sep;65(7):699-702.
To report a new case of secondary bladder amyloidosis, beinginvolvement of the urinary bladder by amyloidosis infrequent on the basis of very few references in the literature (we estimate the number of cases of secondary vesical amyloidosis reported to be around 30).
METHODS/RESULTS: The case presented here corresponds to secondary bladder amyloidosis in a patient suffering from Still's disease, who began with hematuria and ended dying.
Secondary bladder amyloidosis constitutes a very infrequent pathology, and we can distinguish between primary forms of bladder amyloidosis and systemic forms of amyloidosis that affect the urinary bladder (secondary bladder amyloidosis). It is associated in the majority of patients with rheumatoid arthritis that has evolved over a long period. Clinical diagnosis is difficult, and it is necessary to carry out differential diagnosis with bladder tumours. The pathological and immunohistochemical studies confirm the diagnosis.
报告一例继发性膀胱淀粉样变新病例,鉴于文献中相关参考极少(我们估计报告的继发性膀胱淀粉样变病例数约为30例),膀胱受淀粉样变累及的情况并不常见。
方法/结果:此处所呈现的病例为一名患有斯蒂尔病的患者发生的继发性膀胱淀粉样变,该患者以血尿起病,最终死亡。
继发性膀胱淀粉样变是一种非常罕见的病理情况,我们可区分膀胱淀粉样变的原发性形式和累及膀胱的系统性淀粉样变形式(继发性膀胱淀粉样变)。大多数患者与长期演变的类风湿关节炎相关。临床诊断困难,有必要与膀胱肿瘤进行鉴别诊断。病理及免疫组化研究可确诊。