Motoyoshi F, Mori S, Kondo N, Kaneko H, Ozawa T, Kuwabara N, Kato Y, Takemura M, Noma A, Orii T
Department of Pediatrics, Gifu University School of Medicine, Japan.
Scand J Immunol. 1992 Jul;36(1):21-6. doi: 10.1111/j.1365-3083.1992.tb02936.x.
We report a case of common variable immunodeficiency (CVI) that shows low levels of IgG and IgA, but a normal quantitative or qualitative level of IgM. T-cell functions were not disturbed. Increased numbers of surface IgM (sIgM) and sIgD, sIgM and sIgG, sIgM and sIgA double-bearing B cells were observed as compared with a control. No IgG and IgA induction upon stimulation with Staphylococcus aureus Cowan I (SAC) and recombinant interleukin-2 (rIL-2), or pokeweed mitogen (PWM) and rIL-4 or rIL-6 was observed, although there was proliferation. Although mu mRNA was expressed as much as in a healthy control, transcription of gamma mRNA and alpha mRNA was very low. Furthermore, no enhanced effects of gamma mRNA and alpha mRNA were recognized upon stimulation with rIL-4 and rIL-6. These results suggest that the patient's B cells might be defective at the switching process from mu, mu and delta, mu and gamma to gamma or mu and alpha to alpha.
我们报告一例常见变异型免疫缺陷(CVI)病例,该病例显示IgG和IgA水平较低,但IgM的定量或定性水平正常。T细胞功能未受干扰。与对照组相比,观察到表面IgM(sIgM)和sIgD、sIgM和sIgG、sIgM和sIgA双表达B细胞数量增加。在用金黄色葡萄球菌考恩I(SAC)和重组白细胞介素-2(rIL-2),或商陆有丝分裂原(PWM)和rIL-4或rIL-6刺激时,尽管有增殖现象,但未观察到IgG和IgA诱导产生。尽管μ mRNA的表达量与健康对照相同,但γ mRNA和α mRNA的转录非常低。此外,在用rIL-4和rIL-6刺激时,未发现γ mRNA和α mRNA有增强作用。这些结果表明,该患者的B细胞在从μ、μ和δ、μ和γ到γ或从μ和α到α的转换过程中可能存在缺陷。