Carretero Juan, Rissech Miquel, Mortera Carlos, Mayol Javier, Caffarena José, Prada Fredy
Sección de Cardiología Pediátrica, Hospital Sant Joan de Déu-Hospital Clínic, Barcelona, Spain.
Rev Esp Cardiol. 2005 Sep;58(9):1124-6.
We report the case of a male neonate who had a prenatal diagnosis of Fallot's tetralogy. He presented with respiratory distress during the second week of life. Chest x-ray showed an enlarged right ventricle and pulmonary edema. Echocardiography demonstrated characteristic features of Fallot's tetralogy. However, cardiac catheterization disclosed that, in this case of Fallot's tetralogy, the left pulmonary artery had an anomalous origin in the ascending aorta. At 23 days of age, the patient underwent total surgical correction of the defects, during which a direct anastomosis was employed without conduit placement. 10 days later, he was discharged. We present the results of a literature review of the epidemiological, physiopathological, clinical, diagnostic, and surgical characteristics of this rare condition.
我们报告了一例产前诊断为法洛四联症的男性新生儿病例。他在出生后第二周出现呼吸窘迫。胸部X光显示右心室增大和肺水肿。超声心动图显示了法洛四联症的特征性表现。然而,心导管检查发现,在这例法洛四联症病例中,左肺动脉起源于升主动脉,存在异常。患儿23日龄时接受了缺损的完全手术矫正,术中采用直接吻合术,未放置导管。10天后,他出院了。我们呈现了对这种罕见疾病的流行病学、生理病理学、临床、诊断和手术特征的文献综述结果。