Juscinski Jacek, Haponiuk Ireneusz, Chojnicki Maciej, Steffens Mariusz, Szofer-Sendrowska Aneta, Jaworski Radoslaw, Kwasniak Ewelina, Żelechowski Pawel
Department of Pediatric Cardiac Surgery, Pomeranian Centre of Traumatology in Gdansk, Poland.
Department of Pediatric Cardiac Surgery, Pomeranian Centre of Traumatology in Gdansk, Poland ; Department of Pediatric Cardiac Surgery, Pomeranian Centre of Traumatology in Gdansk, Poland.
Kardiochir Torakochirurgia Pol. 2014 Sep;11(3):336-8. doi: 10.5114/kitp.2014.45687. Epub 2014 Sep 28.
Anomalies in development of the pulmonary valve, pulmonary trunk and peripheral pulmonary arteries are typical accompanying pathologies in patients with tetralogy of Fallot (ToF). Demanding for diagnostics and borderline for treatment is a condition colloquially called "discontinuous pulmonary arteries", while the main branches are supplied with systemic blood from the ascending aorta, aortic arch or descending thoracic aorta. We present a case of a one-year-old girl with ToF and anomalous origin of the left pulmonary artery (LPA) from Kommerell's diverticulum who underwent two-stage surgical therapy with the support of interventional cardiology. We conclude that early diagnosis of discontinuous pulmonary artery is crucial for choosing the optimal operative strategy. In our opinion, simultaneous anatomic intracardiac correction with direct pulmonary reconstruction seems reasonable and effective, particularly when the result is achieved after joint efforts of cardiac surgery and interventional cardiology.
肺动脉瓣、肺动脉干及外周肺动脉发育异常是法洛四联症(ToF)患者典型的伴随病变。一种通俗称为“肺动脉中断”的情况对诊断要求较高且治疗存在争议,即主要分支由升主动脉、主动脉弓或胸降主动脉供应体循环血液。我们报告一例1岁患法洛四联症且左肺动脉(LPA)起源于Kommerell憩室的女童,其在介入心脏病学支持下接受了两阶段手术治疗。我们得出结论,肺动脉中断的早期诊断对于选择最佳手术策略至关重要。我们认为,同期进行解剖性心内矫正并直接重建肺动脉似乎合理且有效,尤其是在心脏外科和介入心脏病学共同努力取得成果时。