Neveux J Y, Rioux C, Pernot C, Worms A M, Picchio F, Arpesella G
Arch Mal Coeur Vaiss. 1975 Apr;68(4):405-14.
In relation with the report of two cases of branching of one of the pulmonary arteries from the aorta, it was recalled that this is a rare malformation, responsible for a severe cardiac failure with or without cyanosis in the first months of life, intensly suggestive of a left-to-right shunt. Demonstration of surprizing or unhabitual clinical or haemodynamic findings should indicate the performance of a right-sided angiography then an aortography, this being the only way to secure the diagnosis. Combination of such an anomaly with Fallot's tetralogy is exceptional. The clinical diagnosis is made more difficult by the presence of an anastomosis between the pulmonary and the systemic circulations. Only a careful analysis of right angiograms might make it possible to suspect the presence of an abnormal branching of the pulmonary artery, and to perform the aortography. The treatment is surgical in all cases, and should be undertaken early in life, as it is the only way to control the heart failure or to prevent irreversible pulmonary arteriolar lesions.
关于两例肺动脉之一从主动脉分支的报告,回顾指出这是一种罕见的畸形,在生命的最初几个月可导致严重心力衰竭,伴或不伴有紫绀,强烈提示存在左向右分流。出现令人惊讶或不常见的临床或血流动力学表现时,应先进行右侧血管造影,然后进行主动脉造影,这是确诊的唯一方法。这种异常与法洛四联症合并极为罕见。肺循环与体循环之间存在吻合会使临床诊断更加困难。只有仔细分析右侧血管造影片,才有可能怀疑存在肺动脉异常分支,并进行主动脉造影。所有病例均需手术治疗,且应在生命早期进行,因为这是控制心力衰竭或预防不可逆肺小动脉病变的唯一方法。