Abdulkader M, Abercrombie J, McCulloch T A, Kaye P V
Queens Medical Centre University Hospital, Nottingham NG7 2UH, UK.
J Clin Pathol. 2005 Oct;58(10):1107-9. doi: 10.1136/jcp.2004.025130.
Angiomyolipomas are rare lesions, often arising in the kidney, and are part of a group of tumours with a diverse appearance and evidence of dual melanocytic and smooth muscle differentiation known as PEComas (tumours of perivascular epithelioid cell origin). This report describes an unusual case of a colonic PEComa in a 40 year old woman. Unlike most of the previous colonic angiomyolipomas/PEComas reported in the literature, this case formed a large, mainly extrinsic mass and was monotypic, and composed entirely of the myomatous component with no adipose tissue or typical vasculature.
血管平滑肌脂肪瘤是一种罕见的病变，通常发生于肾脏，是一组外观多样、具有黑素细胞和平滑肌双重分化证据的肿瘤（血管周上皮样细胞瘤）的一部分。本报告描述了一名40岁女性发生结肠血管周上皮样细胞瘤的罕见病例。与文献中报道的大多数既往结肠血管平滑肌脂肪瘤/血管周上皮样细胞瘤不同，该病例形成了一个主要为外生性的大肿块，且为单型，完全由肌瘤成分组成，无脂肪组织或典型脉管系统。
