Mendes Mafalda, Silva Fátima, Simões Luísa, Jorge Marta, Saraiva Jorge, Castelo-Branco Miguel
Centre for Ophthalmology, IBILI, Faculty of Medicine, Az. de Sta Comba, 3000-354 Coimbra, Portugal.
Brain Res Cogn Brain Res. 2005 Dec;25(3):788-98. doi: 10.1016/j.cogbrainres.2005.09.005. Epub 2005 Oct 26.
Williams syndrome (WS) is a neurodevelopmental disorder of genetic origin that has been used as a model to understand visual cognition. We have investigated early deficits in the afferent magnocellular pathway and their relation to abnormal visual dorsal processing in WS. A spatiotemporal contrast sensitivity task that is known to selectively activate that pathway was used in six WS subjects. Additionally, we have compared visual performance in 2D and 3D motion integration tasks. A novel 3D motion coherence task (using spheres with unpredictable axis of rotation) was used in order to investigate possible impairment of occipitoparietal areas that are known to be involved in 3D structure from motion (SFM) perception. We have found a significant involvement of low-level magnocellular maps in WS as assessed by the contrast sensitivity task. On the contrary, no significant differences were observed between WS and the control groups in the 2D motion integration tasks. However, all WS subjects were significantly impaired in the 3D SFM task. Our findings suggest that magnocellular damage may occur in addition to dorsal stream deficits in these patients. They are also consistent with recently described genetic and neuroanatomic abnormalities in retinotopic visual areas. Finally, selective SFM coherence deficits support the proposal that there is a specific pathway in the dorsal stream that is involved in motion processing of 3D surfaces, which seems to be impaired in this disorder.
威廉姆斯综合征(WS)是一种遗传性神经发育障碍,已被用作理解视觉认知的模型。我们研究了传入大细胞通路的早期缺陷及其与WS中异常视觉背侧加工的关系。在6名WS受试者中使用了一种已知能选择性激活该通路的时空对比敏感度任务。此外,我们比较了2D和3D运动整合任务中的视觉表现。为了研究已知参与从运动感知3D结构(SFM)的枕顶叶区域可能存在的损伤,使用了一种新颖的3D运动连贯性任务(使用具有不可预测旋转轴的球体)。通过对比敏感度任务评估,我们发现WS中低水平大细胞图谱有显著参与。相反,在2D运动整合任务中,WS组与对照组之间未观察到显著差异。然而,所有WS受试者在3D SFM任务中均有显著损伤。我们的研究结果表明,除了这些患者的背侧流缺陷外,可能还存在大细胞损伤。它们也与最近描述的视网膜视觉区域的基因和神经解剖学异常一致。最后,选择性SFM连贯性缺陷支持了这样一种观点,即背侧流中存在一条特定的通路参与3D表面的运动处理,而这种疾病似乎会损害该通路。