Song Jae-Jun, Jung Hak-Hyun, Lee Heung-Man, Hwang Soon-Jae
Department of Otorhinolaryngology-Head and Neck Surgery, Korea University College of Medicine, Seoul, South Korea.
Acta Otolaryngol. 2005 Oct;125(10):1126-9. doi: 10.1080/00016480510035430.
Fibrous dysplasia is a bone disorder of unknown origin characterized by slow, progressive replacement of bone by abnormal proliferative isomorphic fibrous tissue. The disease was first described by McCune and Bruch in 1937. Craniofacial involvement is found in only 10% of cases of the monostotic variety, while temporal bone involvement is rare. We report herein two cases of monostotic fibrous dysplasia involving temporal bone and briefly review the clinical implications and management of the disease.
骨纤维异常增殖症是一种病因不明的骨疾病,其特征是异常增殖的同形纤维组织缓慢、渐进性地替代骨组织。该疾病于1937年由麦库恩和布鲁赫首次描述。单骨型病例中仅有10%出现颅面部受累,而颞骨受累罕见。我们在此报告两例累及颞骨的单骨型骨纤维异常增殖症病例,并简要回顾该疾病的临床意义及治疗。