Ryu Dong Yup, Hwang Sang Youn, Lee Dong Won, Kim Tae Oh, Park Do Youn, Kim Gwang Ha, Heo Jeong, Kang Dae Hwan, Song Geun Am, Cho Mong
Department of Internal Medicine, Pusan National University College of Medicine, Busan, Korea.
Korean J Gastroenterol. 2005 Nov;46(5):404-8.
Angiosarcoma is a rare malignant tumor which occurs frequently in the skin and soft subcutis. Moreover, primary gastrointestinal angiosarcomas are very rare. This tumor manifests as non-specific symptoms such as gastrointestinal bleeding, abdominal pain and nausea. The diagnosis is often made at an advanced stage. Surgery, chemotherapy and radiotherapy are the mainstay of treatment. However, the prognosis is very poor. We report a case of primary angiosarcoma of the small intestine presenting as recurrent gastrointestinal bleeding. A 54-year-old man was admitted with recurrent gastrointestinal bleeding. An abdominal CT scan revealed an ileo-ileal intussusception. Segmental resection was performed with ileo-ileal anastomosis. The ileal mass was diagnosed as angiosarcoma on immunohistochemical stain. He received 3 cycles of chemotherapy, but died 5 months after the diagnosis.
血管肉瘤是一种罕见的恶性肿瘤,常发生于皮肤和皮下软组织。此外,原发性胃肠道血管肉瘤极为罕见。该肿瘤表现为非特异性症状,如胃肠道出血、腹痛和恶心。诊断通常在疾病晚期做出。手术、化疗和放疗是主要的治疗方法。然而,预后非常差。我们报告一例以反复胃肠道出血为表现的原发性小肠血管肉瘤病例。一名54岁男性因反复胃肠道出血入院。腹部CT扫描显示回肠套叠。行节段性切除并回肠吻合术。回肠肿物经免疫组化染色诊断为血管肉瘤。他接受了3个周期的化疗,但在诊断后5个月死亡。