婴儿促纤维增生性幕上神经上皮肿瘤

Desmoplastic supratentorial neuroepithelial tumours of infancy.

作者信息

Paulus W, Schlote W, Perentes E, Jacobi G, Warmuth-Metz M, Roggendorf W

机构信息

Institute of Pathology, University of Würzburg, Germany.

出版信息

Histopathology. 1992 Jul;21(1):43-9. doi: 10.1111/j.1365-2559.1992.tb00341.x.

DOI:10.1111/j.1365-2559.1992.tb00341.x

PMID:1634201

Abstract

The clinicopathological features of two infants with desmoplastic supratentorial neuroepithelial tumours are described. The cases were similar to the 26 cases reported previously as desmoplastic infantile ganglioglioma and superficial cerebral astrocytoma attached to dura. Neuronal differentiation was absent on routine stains, but was immunohistochemically established. We review the literature and suggest classifying this clinicopathological entity by using a general designation such as desmoplastic supratentorial neuroepithelial tumours of infancy, a term which indicates the variability in the amount and lines of differentiation.

摘要

本文描述了两名患有促结缔组织增生性幕上神经上皮肿瘤婴儿的临床病理特征。这些病例与之前报道的26例促结缔组织增生性婴儿型节细胞胶质瘤和附着于硬脑膜的浅表性脑星形细胞瘤相似。常规染色未见神经元分化，但免疫组化确定存在神经元分化。我们回顾了文献，并建议使用一个通用名称来对这种临床病理实体进行分类，如婴儿促结缔组织增生性幕上神经上皮肿瘤，该术语表明了分化程度和分化谱系的变异性。