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儿童播散性黄瘤伴肝脏受累

Xanthoma disseminatum with hepatic involvement in a child.

作者信息

Büyükavci Mustafa, Selimoglu Ayse, Yildirim Umran, Ertekin Vildan, Atasoy Mustafa

机构信息

Division of Pediatric Oncology, Ataturk University, Faculty of Medicine, Erzurum, Turkey.

出版信息

Pediatr Dermatol. 2005 Nov-Dec;22(6):550-3. doi: 10.1111/j.1525-1470.2005.00138.x.

Abstract

Xanthoma disseminatum is a rare, usually self-healing dermatologic disease of unknown etiology. Involvement of other organs and tissues including bone marrow, bone, and brain may be seen rarely in children. However, to date, hepatic involvement has not been reported. We describe a child with xanthoma disseminatum who had hepatic involvement, and discuss his course and treatment with steroid and azathioprine.

摘要

播散性黄瘤是一种病因不明的罕见的、通常可自愈的皮肤病。儿童中很少见其他器官和组织受累,包括骨髓、骨骼和脑。然而,迄今为止,尚未有肝脏受累的报道。我们描述了一名患有播散性黄瘤且有肝脏受累的儿童,并讨论了其病情过程以及使用类固醇和硫唑嘌呤的治疗情况。

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