伴有体循环侧支供血的布兰德-怀特-加兰综合征长期存活者：一例病例报告及文献复习
A long-term survivor of Bland-White-Garland syndrome with systemic collateral supply: a case report and review of the literature.
作者信息
Barbetakis N, Efstathiou A, Efstathiou N, Papagiannopoulou P, Soulountsi V, Fessatidis I
机构信息
Cardiothoracic Surgery Department, Geniki Kliniki, Thessaloniki, Greece.
出版信息
BMC Surg. 2005 Dec 15;5:23. doi: 10.1186/1471-2482-5-23.
BACKGROUND
Bland-White-Garland syndrome (anomalous origin of the left coronary artery from the pulmonary artery) is a rare disease which may result in myocardial infarction, congestive heart failure and sometimes death during the early infantile period.
CASE PRESENTATION
A successfully treated case of a 45-year-old mother of 2 children with Bland-White-Garland syndrome and concomitant severe mitral regurgitation is presented. Subsequent therapy consisted of ligation of the anomalous origin of the left coronary artery, anastomosis of the left internal mammary artery to the left anterior descending branch and mitral valve replacement. Continuous blood flow from the left coronary artery ostium during extracorporeal circulation and aorta clamping suggested systemic collateral supply.
CONCLUSIONS
Recognition and diagnosis of Bland-White-Garland syndrome is important due to its potentially life-threatening complications.
背景
布兰德-怀特-加兰综合征（左冠状动脉起源于肺动脉异常）是一种罕见疾病，可能导致婴儿早期心肌梗死、充血性心力衰竭，有时甚至死亡。
病例报告
本文介绍了一例成功治疗的病例，患者为一位育有2个孩子的45岁母亲，患有布兰德-怀特-加兰综合征并伴有严重二尖瓣反流。后续治疗包括结扎左冠状动脉异常起源、将左乳内动脉吻合至左前降支以及二尖瓣置换。体外循环和主动脉夹闭期间左冠状动脉口持续有血流，提示存在体循环侧支供血。
结论
由于布兰德-怀特-加兰综合征可能引发危及生命的并发症，因此对其进行识别和诊断很重要。
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