Premalata C S, Kumar Rekha V, Appaji L, Prabhakaran P S
Department of Pathology, Kidwai Memorial Institute of Oncology, M.H. Marigowda Road, Bangalore.
Indian J Pathol Microbiol. 2005 Oct;48(4):487-9.
Hepatic angiosarcoma (HAS) is an extremely rare liver tumor in children. We report a case of childhood HAS in a six year old girl who presented with acute abdominal pain and fever with a mass in epigastrium. Left hepatic lobectomy was performed with a clinical diagnosis of hepatoblastoma. Histopathological examination revealed features typical of hepatic angiosarcoma. The case is presented for its rarity and to discuss the interrelation between infantile hemangioendothelioma (IHE) and HAS.
肝血管肉瘤(HAS)是儿童中极为罕见的肝脏肿瘤。我们报告一例6岁女童患儿童期HAS的病例,该患儿表现为急性腹痛、发热,上腹部有肿块。临床诊断为肝母细胞瘤并行左肝叶切除术。组织病理学检查显示为典型的肝血管肉瘤特征。本文报告该病例是因其罕见性,并讨论婴儿型血管内皮瘤(IHE)与HAS之间的相互关系。