Pethe V V, Kalgutkar A D, Mondkar J, Oak S N, Deodhar K P, Deshmukh S S
Department of Pathology, Lokmanya Tilak Municipal Medical College and Hospital, Sion, Bombay, India.
Indian J Cancer. 1995 Dec;32(4):186-8.
A case of infantile hemangioendothelioma of the liver is reported in a 18 day-old male neonate. The neonate presented with CHF. He had hepatomegaly, but lacked the third component of the classical triad i.e. cutaneous hemangiomas. The S.A.F.P levels were raised to 920 ng/ml, though rise is rare in infantile hemangioendothelioma and led to the clinical diagnosis of hepatoblastoma. A left hepatic resection was performed, the histology showed a type I pattern of the tumor. This is known to be associated with a good prognosis. The baby is well post resection for a follow up period of six months.
本文报告了一例18日龄男性新生儿的肝脏婴儿型血管内皮瘤。该新生儿表现为充血性心力衰竭。他有肝肿大,但缺乏经典三联征的第三个组成部分,即皮肤血管瘤。血清甲胎蛋白水平升高至920 ng/ml,尽管婴儿型血管内皮瘤中这种升高很少见,这导致了肝母细胞瘤的临床诊断。进行了左肝切除术,组织学显示为I型肿瘤。已知这种类型与良好的预后相关。术后随访六个月,婴儿情况良好。