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[系统性红斑狼疮伴出血性心包炎及心脏压塞。病例报告]

[Hemorrhagic pericarditis and cardiac tamponade in systemic lupus erythematosus. A case report].

作者信息

Barrera-Ramírez Carlos Felipe, Pineda-Pompa Luis R, Melo Mario, Valdez Castro Ricardo, Medina-Gómez Héctor, Godina-Alonso Gustavo, Guzmán Carlos E

机构信息

Departamento de Cardiología Intervencionista y Hemodinamia, División Cardiovascular, Centro Hospitalario la Concepción, Blvd. V. Carranza Núm. 4036, c.p. 25230 Saltillo, Coah., México.

出版信息

Arch Cardiol Mex. 2005 Jul-Sep;75 Suppl 3:S3-96-9.

Abstract

Systemic lupus erythematosus is a chronic inflammatory autoimmune disorder that can affect any organ or system. Although pericarditis is the most frequent cardiac manifestation of this entity, usually is not a life threatening situation. Pericardial effusion causing cardiac tamponade is a very rare complication in lupus, with an incidence less than 2%. We report a case of pericardial tamponade due to SLE with severe hemodynamic involvement in a 21-year-old woman associated to rapidly progressive glomerulonephritis, acute pancreatitis, acute acalculous cholecystitis, pleural effusion, hematologic, cutaneous and neurologic lupus activity. Recognition of this rare manifestation of SLE may be life saving.

摘要

系统性红斑狼疮是一种慢性炎症性自身免疫性疾病,可影响任何器官或系统。虽然心包炎是该疾病最常见的心脏表现,但通常并非危及生命的情况。狼疮性心包积液导致心脏压塞是一种非常罕见的并发症,发生率低于2%。我们报告一例21岁女性因系统性红斑狼疮导致心脏压塞,伴有严重血流动力学受累,并伴有快速进展性肾小球肾炎、急性胰腺炎、急性非结石性胆囊炎、胸腔积液、血液学、皮肤和神经狼疮活动。认识到系统性红斑狼疮的这种罕见表现可能会挽救生命。

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