Cigarroa López José Angel, García Jiménez Yoloxóchitl, Yáñez Gutiérrez Lucelly, Jiménez Arteaga Santiago, Martínez Sánchez Arturo, Ortegón Cardeña José, Gómez Felipe David, Sánchez Soberanes Agustín, López Gallegos Diana, Riera-Kinkel Carlos, Alva Espinosa Carlos
Servicio de Cardiopatías Congénitas, Hospital de Cardiología, Centro Médico Nacional Siglo XXI, Delegación Cuauhtémoc, México, Distrito Federal.
Arch Cardiol Mex. 2005 Jul-Sep;75 Suppl 3:S3-113-7.
The primary cardiac tumors are inusual, the incidence varies in all the ages between 0.005 to 0.05%. In pediatrics patients the incidence is 0.27%. The more frequent tumors during the childhood are the cardiac rhabdomyomas. These tumors are considered benigns. The clinical expression is wide, in the most the cases, the patients are asymptomatic and are detected by murmurs. In the prenatal age are manifested by arrhythmias or hydrops fetalis. The neonates and children may be show cardiac arrhythmias, low cardiac index and sudden cardiac death. The association with tuberous sclerosis had been reported in 81%. We present a neonate with cardiac rhabdomyoma diagnosed in the newborn period when he was asymptomatic, however in the follow-up he developed cardiac failure by obstruction in the out flow tract of the right ventricle. He underwent open cardiac surgery to resect the obstruction. Five months after surgery, the patient remain asymptomatic.
原发性心脏肿瘤较为罕见,其发病率在各年龄段为0.005%至0.05%不等。在儿科患者中,发病率为0.27%。儿童期最常见的肿瘤是心脏横纹肌瘤。这些肿瘤被认为是良性的。临床表现广泛,在大多数情况下,患者无症状,通过杂音被发现。在胎儿期表现为心律失常或胎儿水肿。新生儿和儿童可能出现心律失常、低心指数和心源性猝死。据报道,81%的病例与结节性硬化症有关。我们报告一例新生儿,在新生儿期被诊断为心脏横纹肌瘤,当时无症状,但在随访中因右心室流出道梗阻发展为心力衰竭。他接受了心脏直视手术以切除梗阻。术后五个月,患者仍无症状。