Ozbek Baburhan, Gunes Ayhan, Ozturker Kenan, Faruk Savluk Omer, Cevirme Deniz, Tuncer Eylem
Department of Pediatric Cardiovascular Surgery, Kosuyolu Training and Research Hospital, Istanbul, Türkiye.
Department of Cardiovascular Surgery, Kosuyolu Training and Research Hospital, Istanbul, Türkiye.
Sisli Etfal Hastan Tip Bul. 2024 Sep 30;58(3):395-397. doi: 10.14744/SEMB.2024.50460. eCollection 2024.
Cardiac rhabdomyoma is the most common primary cardiac tumor in infants and can be diagnosed by fetal echocardiography. This benign tumor can be found in various locations within the heart, including the left ventricle, right ventricle, or septum, and is typically multiple. While spontaneous regression may occur, hemodynamic disorders, arrhythmias, and sudden death have also been reported. Surgical treatment is recommended for life-threatening ventricular outflow tract stenosis, heart failure, and arrhythmias. This case report presents a successful surgical treatment approach in a newborn with rhabdomyoma that caused severe left ventricular outflow tract stenosis.
心脏横纹肌瘤是婴儿最常见的原发性心脏肿瘤,可通过胎儿超声心动图诊断。这种良性肿瘤可在心脏内的不同部位发现,包括左心室、右心室或室间隔,且通常为多发性。虽然可能会发生自发消退,但也有血流动力学紊乱、心律失常和猝死的报道。对于危及生命的心室流出道狭窄、心力衰竭和心律失常,建议进行手术治疗。本病例报告介绍了一名患有导致严重左心室流出道狭窄的横纹肌瘤的新生儿的成功手术治疗方法。